Pulmonary arterovenous malformation causing hemothorax in a pregnant woman without Osler-Weber-Rendu syndrome
نویسندگان
چکیده
Pulmonary arteriovenous malformations (PAVMs), although most commonly congenital, are usually detected later in life. CASE REPORT We present a case of a 19-year-old woman with no previous history of AVM or telangiectasia, who presented dyspnea and hypoxia by massive left hemothorax in the 34th week of gestation. After emergent cesarean delivery, a chest computed tomography (CT) with i.v. contrast showed a likely 3 cm area of active contrast in left lower lung. Chest tube placement revealed about 2 liters of blood. The patient was subsequently found to have pulmonary AVM. A successful embolisation of AVM followed by lung atipic resection involving AVM and decortication for lung re-expansion were the treatments provided. CONCLUSIONS Women with known pulmonary AVM should be maximally treated prior to becoming pregnant, and the physician should be alert to complications of pulmonary AVM during pregnancy.
منابع مشابه
Osler-Rendu-Weber syndrome: congenital arteriovenous intrapulmonary fistula treated using a percutaneous Amplatzer plug.
Pulmonary arteriovenous fistulas (PAVFs) are rare vascular malformations (PAVMs) of the lung that could lead to severe hypoxiemia due to right-to-left intrapulmonary shunts. They may occur as isolated entities or associated with Osler-Rendu-Weber syndrome or hereditary haemorrhagic telangiectasia (HHT). We report a case of a 70 years old woman with Rendu-Osler-Weber disease and a large arteriov...
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Hereditary haemorrhagic telangiectasia (OslerWeber-Rendu disease) is an uncommon disease and, in over 98% of cases, the patients present with recurrent episodes of epistaxis (Harrison, 1964). It has been estimated that 15% of patients develop a pulmonary arterio-venous fistula during their lives (Hodgson et al., 1959). The patient with a pulmonary arterio-venous fistula may suffer from various ...
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